TITLE:
Primary Cardiac Rhabdomyosarcoma in a Child—A Case Report
AUTHORS:
Krishna Prasad Maram, Vikram Kudumula, Dilip Ratti, Sindhura Paturi
KEYWORDS:
Rhabdomyosarcoma, Pericardial Effusion, Sternotomy
JOURNAL NAME:
World Journal of Cardiovascular Surgery,
Vol.11 No.2,
February
26,
2021
ABSTRACT: Unlike benign primary cardiac tumors like rhabdomyomas and fibromas, primary malignant tumors are extremely rare in children with very few cases reports in the literature so far. Rhabdomyosarcoma is a rare primary malignant tumor in children with most reported cases occurring in the right heart. We report a 15-month-old child with a primary rhabdomyosarcoma arising from the left ventricle and presenting with cardiac tamponade and circulatory failure. He underwent a diagnostic sternotomy and palliative chemotherapy but succumb to the disease later.