TITLE:
Early Ophthalmological Manifestations of Crouzon Syndrome: About a Case
AUTHORS:
Nidain Maneh, Meba Banla, Nadiedjoa Kokou Douti, Komi Yayehd, Sophie Arsene, Kokou Vonor, Kassoula Batomaguela Nonon Saa, Koffi Didier Ayena, Komi Patrice Balo
KEYWORDS:
Craniofacial Dysostosis
JOURNAL NAME:
Open Access Library Journal,
Vol.1 No.7,
October
30,
2014
ABSTRACT: We report the case of a major neonatal form of Crouzon syndrome of ophthalmic finding in a new-born of 21 days of age with no background of consanguinity. The clinical manifestations were marked by signs of Crouzon syndrome associated with dyspnea. The skull radiograph showed a decline of maxillary and closing sutures. The brain scan was marked by a bilateral fronto-parietal hypotrophy with agnenesis of the left temporal. She had received a lateral tarsorrhaphy in prevention to keratopathy of exposure. We noted a substantive consideration of normal eye and no recurrence throttle of eyeball 6 months after tarsorrhaphy. The major forms of Crouzon syndrome is a source of complications including exposure keratopathy and optic atrophy requiring ophthalmological caring in awaiting for a craniofacial surgery.