TITLE:
A Primary Epithelioid Hemangioendothelioma of the Right Atrium: Report of a Case and Literature Review
AUTHORS:
Tsutomu Sugimoto, Kazuo Yamamoto, Shinpei Yoshii
KEYWORDS:
Epithelioid Hemangioendothelioma; Heart; Right Atrium
JOURNAL NAME:
Open Journal of Thoracic Surgery,
Vol.3 No.2,
June
5,
2013
ABSTRACT:
Primary cardiac epithelioid hemangioendothelioma (EHE) is extremely uncommon. To our knowledge, only fourteen cases have been reported. We report a case of a primary EHE of the right atrium which incidentally detected in 77-year-old woman. Echocardiograhpy revealed a 26 × 16 mm right atrial mass attached to the base of the interatrial septum and moderate regurgitation of the tricuspid valve. The tumor and stalk were completely resected from the interatrial septum with a partial resection of the septal leaflet of the tricuspid valve. The patient had an uneventful postoperative course and no signs of recurrence nor metastasis of EHE 4 years after operation. Because of malignant potential of EHE, a longer period of close follow up is necessary.