Deshayes, S., Aouba, A., Khoy, K., Mariotte, D., Lobbedez, T. and Martin Silva, N. (2018) Hypocomplementemia Is Associated with Worse Renal Survival in ANCA-Positive Granulomatosis with Polyangiitis and Microscopic Polyangiitis. PLoS ONE, 13, e0195680.
https://doi.org/10.1371/journal.pone.0195680

has been cited by the following article:

• TITLE: An Unusual Case of a Pulmonary-Renal Syndrome with Negative Anti-GBM and ANCA Antibodies

  AUTHORS: Fabrício Malaguez Webber, Edson Ricardo Junior, Maria Belen López Morillo, Emanuel Malaguez Webber

  KEYWORDS: Pulmonary Renal Syndrome, Goodpasture, ANCA, Anti-GBM

  JOURNAL NAME: Case Reports in Clinical Medicine, Vol.7 No.8, August 9, 2018

  ABSTRACT: Pulmonary renal syndrome (PRS) is a high mortality, rare disorder presenting with diffuse alveolar hemorrhage and progressive acute glomerulonephritis. This syndrome is often caused by autoimmune entities, the most frequent being ANCA positive vasculitis and anti-GBM disease. We report a case of a 34-year-old Chilean woman, who initially presents with anemia and after a few days of inpatient management, starts with progressively worsening dyspnea, decrease in renal function and hematuria. The patient is initially diagnosed with pneumonia, but further evaluation using Thorax CT scan and renal biopsy confirms the suspicion of PRS. The case is of particular interest due to the lack of extensive bibliography on anti-GBM and ANCA negative pulmonary-renal syndrome, an uncategorized subtype of this syndrome with unknown optimal management.