Early Ophthalmological Manifestations of Crouzon Syndrome: About a Case

Nidain Maneh^1*, Meba Banla¹, Nadiedjoa Kokou Douti², Komi Yayehd³, Sophie Arsene⁴, Kokou Vonor¹, Kassoula Batomaguela Nonon Saa¹, Koffi Didier Ayena¹, Komi Patrice Balo¹

¹Eye Department chu Campus, University of Lomé, Lomé, Togo.
²Department of Paediatric chu Campus, University of Lomé, Lomé, Togo.
³Heart Department chu Campus, Lomé, Togo.
⁴Eye Department chu, Tours, France.

DOI: 10.4236/oalib.1101046                

Abstract

We report the case of a major neonatal form of Crouzon syndrome of ophthalmic finding in a new-born of 21 days of age with no background of consanguinity. The clinical manifestations were marked by signs of Crouzon syndrome associated with dyspnea. The skull radiograph showed a decline of maxillary and closing sutures. The brain scan was marked by a bilateral fronto-parietal hypotrophy with agnenesis of the left temporal. She had received a lateral tarsorrhaphy in prevention to keratopathy of exposure. We noted a substantive consideration of normal eye and no recurrence throttle of eyeball 6 months after tarsorrhaphy. The major forms of Crouzon syndrome is a source of complications including exposure keratopathy and optic atrophy requiring ophthalmological caring in awaiting for a craniofacial surgery.

Keywords

Craniofacial Dysostosis

Conflicts of Interest

The authors declare no conflicts of interest.

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