Malignant Triton Tumor in the Abdominal Wall: A Case Report


Malignant triton tumor (MTT) is a rare variant of malignant peripheral nerve sheath tumor (MPNST) with rhabdomyosarcomatous differentiation. We report the case of a 54-year-old male without a history of neurofibromatosis type 1 (NF1) who had a growing abdominal wall tumor diagnosed as MTT. Computed tomography (CT), magnetic resonance imaging (MRI) and 2-[F-18]-fluoro-2-deoxy-D-glucose positron emission tomography/CT (FDG-PET/CT) were performed. The MRI and FDG-PET/CT indicated that the lateral component of the tumor was composed of many proliferative cells, corresponding to the histopathological finding of a cellular proliferation of spindle-shaped cells. In light of this case and previous reports, it is apparent that FDG-PET/CT is a helpful tool for distinguishing MTT from benign peripheral nerve sheath tumor.

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Y. Kitamura, K. Abe, S. Baba, T. Isoda, Y. Maruoka, Y. Matsuo, Y. Kubo, A. Sakamoto, H. Nishimura, M. Sasaki and H. Honda, "Malignant Triton Tumor in the Abdominal Wall: A Case Report," Advances in Molecular Imaging, Vol. 3 No. 2, 2013, pp. 9-13. doi: 10.4236/ami.2013.32002.

Conflicts of Interest

The authors declare no conflicts of interest.


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