Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome
Kelly Zach, Lopa Misra
Mayo Clinic Hospital, Phoenix, AZ, USA.
DOI: 10.4236/ojanes.2015.52007   PDF    HTML   XML   4,483 Downloads   5,602 Views   Citations


Hermansky-Pudlak Syndrome (HPS) is a rare genetic condition characterized by platelet function abnormalities and oculocutaneous albinism. Other systemic manifestations of the disease include pulmonary fibrosis, granulomatous colitis, impaired renal function, and cardiomyopathy. Due to the systemic extent of the disease, HPS has multiple anesthetic concerns and requires a detailed preoperative evaluation and close perioperative monitoring.

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Zach, K. and Misra, L. (2015) Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome. Open Journal of Anesthesiology, 5, 33-36. doi: 10.4236/ojanes.2015.52007.

Conflicts of Interest

The authors declare no conflicts of interest.


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