Pneumonectomy in a Patient with Swyer-James-MacLeod Syndrome

DOI: 10.4236/ss.2015.62009   PDF   HTML   XML   3,559 Downloads   4,076 Views   Citations

Abstract

Swyer-James-MacLeod syndrome is a rare disease that results in parenchymal damage believed to be caused by recurrent lung infections in childhood. We report a case of a previously healthy young woman that presented with insidious progression of exertional dyspnea with restrictive lung physiology. Axial imaging demonstrated a hyperinflated emphysematous right lung with lower lobe fibrosis, nodules and air-fluid filled cysts, with a small right pulmonary artery and contralateral shifting of the mediastinum. She underwent right pneumonectomy ultimately resulting in improvement of her symptoms, with surgical pathology indicating extensive emphysema, bronchiec- tasis, fibrosis with osseous metaplasia, and placental transmogrification of alveolar septa, being consistent with a diagnosis of SJMS.

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Cruz, M. and Trachiotis, G. (2015) Pneumonectomy in a Patient with Swyer-James-MacLeod Syndrome. Surgical Science, 6, 55-58. doi: 10.4236/ss.2015.62009.

Conflicts of Interest

The authors declare no conflicts of interest.

References

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[2] Macleod, W.M. (1954) Abnormal Transradiency of One Lung. Thorax, 9, 147-153.
http://dx.doi.org/10.1136/thx.9.2.147
[3] da Silva, P.S., Lopes, R. and Neto, H.M. (2012) Swyer-James-MacLeod Syndrome in a Surgically Treated Child: A Case Report and Brief Literature Review. Journal of Pediatric Surgery, 47, e17-e22.
[4] Vishnevsky, A. and Nikoladze, G. (1990) New Approach to the Surgical Treatment of Swyer-James-MacLeod Syndrome. The Annals of Thoracic Surgery, 50, 130-134. http://dx.doi.org/10.1016/0003-4975(90)90098-Q
[5] Marchevsky, A., Guintu, R., et al. (2005) Swyer-James (MacLeod) Syndrome with Placental Transmogrification of the Lung: A Case Report and Review of the Literature. Archives of Pathology & Laboratory Medicine, 129, 686-689.

  
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