Our Experience with Embryonal Rhabdomyosarcoma Presenting as Aural Polyp

Anoop Attakkil, Vandana Thorawade, Mohan Jagade, Rajesh Kar, Dnyaneswar Rohe, Reshma Hanowate, Devkumar Rangaraja, Kartik Parelkar

Department of ENT, Grant Medical College & Sir J.J. Hospital, Mumbai, India.

DOI: 10.4236/ijohns.2015.41001                

Abstract

Aural polyps are a common clinical entity encountered by otorhinolaryngologist in daily practice. Polyps are frequently seen in paediatric patients, usually inflammatory in nature. In children rhabdomyosarcomas (RMS) can mimic all the cinical features of chronic suppurative otitis media which usually present as external auditory canal mass or polyp. Here we present a case where a male child presented with recurrence of polyp in left ear which was finally diagnosed as embryonal rhabdomyosarcoma which is a rare and invariably fatal disease in children. Through this article we intend to highlight the failures and delay committed in attaining diagnosis in this patient in spite of multispecialty evaluation involving repeated imaging and histopathological correlation. Our experience with embryonal rhabdomyosarcoma throws light on the high vigilance required in handling the aural polyps in pediatric population as early diagnosis and treatment are the key elements for successful outcomes.

Keywords

Embryonal Rhabdomyosarcoma, Aural Polyp, CSOM

Conflicts of Interest

The authors declare no conflicts of interest.

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