Successful Tacrolimus Therapy Extended by Everolimus in Retroperitoneal Angiomyolipoma after Lung Transplantation: A Case Report

Lymphangioleiomyomatosis (LAM) is a rare disease that affects women, especially in child-bearing age. Clinical manifestations include angiomyolipoma, pneumothorax, chylothorax, cystic changes of lungs and progressive pulmonary failure. In this article, we report a case of lung transplantation (LuTX) for end stage pulmonary LAM and the treatment of angiomyolipoma showing growth after LuTX resulting in complete remission with combination therapy of everolimus and tacrolimus.

KEYWORDS

Lymphangioleiomyomatosis, Everolimus, Angiomyolipoma, Lung Transplant

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Erdélyi, T. , Bohács, A. , Vincze, K. , Kováts, Z. , Sárosi, V. , Sinkovicz, A. , Balázs, G. and Müller, V. (2014) Successful Tacrolimus Therapy Extended by Everolimus in Retroperitoneal Angiomyolipoma after Lung Transplantation: A Case Report. Case Reports in Clinical Medicine, 3, 636-638. doi: 10.4236/crcm.2014.312135.

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