Successful Tacrolimus Therapy Extended by Everolimus in Retroperitoneal Angiomyolipoma after Lung Transplantation: A Case Report

Tamás Erdélyi¹, Anikó Bohács¹, Krisztina Vincze¹, Zsuzsanna Kováts¹, Veronika Sárosi², András Sinkovicz², György Balázs³, Veronika Müller¹

¹Department of Pulmonology, Semmelweis University, Budapest, Hungary.
²1st Department of Internal Medicine, Medical School, University of Pécs, Pécs, Hungary.
³Department of Radiology, The Heart and Vascular Center, Semmelweis University, Budapest, Hungary.

DOI: 10.4236/crcm.2014.312135                

Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease that affects women, especially in child-bearing age. Clinical manifestations include angiomyolipoma, pneumothorax, chylothorax, cystic changes of lungs and progressive pulmonary failure. In this article, we report a case of lung transplantation (LuTX) for end stage pulmonary LAM and the treatment of angiomyolipoma showing growth after LuTX resulting in complete remission with combination therapy of everolimus and tacrolimus.

Keywords

Lymphangioleiomyomatosis, Everolimus, Angiomyolipoma, Lung Transplant

Conflicts of Interest

The authors declare no conflicts of interest.

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