Aggressive angiomyxoma pelvis presenting as an ovarian tumor

Errarhay Sanaa, Lamquami Safae, Mahmoud Samia, El Fatemi Hinde, Saadi Hanane, Squalli Nadia, Bouchikhi Chahrazed, Amarti Afaf, Banani Abdelaziz

Department of Pathology, University Hospital of Fez, Fez, Morocco.
Department of Qynecology and Obstetrics, University Hospital of Fez, Fez, Morocco.
Department of Radiology, University Hospital of Fez, Fez, Morocco.

DOI: 10.4236/ojog.2013.38111                

Abstract

Aggressive angiomyxoma is rare mesenchymal tumor that most commonly arises in the vulvo-vaginal region, perineum, and pelvis of women. The term aggressively emphasizes the often infiltrative nature of the tumor and its frequent association with local recurrence. Preoperative diagnosis and treatment may be difficult. We report a 55-year-old patient who presented with a pelvic mass with no significant medical history. The radiological assessment showed a pelvic cystic tumor retro and lateral bladder. A surgical excision was performed with a diagnosis of aggressive angiomyxoma pelvis that misdiagnosed as ovarian tumor. The patient received adjuvant radiotherapy after surgery and remains well with no signs of local recurrence at 12 months follow-up. As surgery is the main treatment, preoperative diagnosis and assessment of extent of the tumor for planning surgery can not be overemphasized. The authors discuss this finding through the diagnostic difficulties and the evolution of this entity.

Keywords

Aggressive Angiomyxoma; Pelvic Neoplasm; Immunohistochemistry

Conflicts of Interest

The authors declare no conflicts of interest.

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