A case report on retroperitoneal PNET/EWS


Primitive neuroectodermal tumor (PNET) and Ewing’s sarcoma (EWS) are small round cell tumors occurring mainly in children and adolescents, rarely in adults. It can occur in multiple tissues and organs including kidney, adrenal, bladder, liver, small intestine, colon and rectum, with a preferred location within the chest area, in the limbs and around the spine, but with rare cases of abdominal, pelvic or retroperitoneal. Here we present a case of the retroperitoneal PENT/EWS in a 38-year-old man and we discuss the clinical features, histopathological characteristics, diagnosis, treatment and prognosis.

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Zhang, Z. , Yu, H. , Shi, Y. and Shi, H. (2013) A case report on retroperitoneal PNET/EWS. Case Reports in Clinical Medicine, 2, 366-369. doi: 10.4236/crcm.2013.26098.

Conflicts of Interest

The authors declare no conflicts of interest.


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