Hypergammaglobulinemic purpura of waldenstorm associated with sjogren’s syndrome in a young female responding to rituximab treatment

Neeraj Jain, Lalit Duggal

Department of Rheumatology & Clinical Immunology, Sir Ganga Ram Hospital, New Delhi, India;.

DOI: 10.4236/crcm.2013.22034                

Abstract

Hypergammaglobulinemic Purpura of Waldenstorm is one of the uncommon conditions with purpura and is often associated with collagen vascular disease. It is difficult to treat and sometimes needs anti CD 20 molecules for resistant cases.

Keywords

Hypergammaglobulinemic Purpura of Waldenstorm; Sjogren’s Syndrome; Rituximab

Conflicts of Interest

The authors declare no conflicts of interest.

References

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