Incidental Finding of Isolated Rosai-Dorfman Disease in the Tonsils of a 4-Year-Old Girl: A Case Report and a Brief Review of Current Practice in Tonsillectomy Specimen Handling

Julianne Qualtieri, Samir B. Kahwash

Department of Pathology and Laboratory Medicine, Nationwide Children’s Hospital, Columbus, USA.
Department of Pathology, The Ohio State University, Columbus, USA.

DOI: 10.4236/ojpathology.2013.31002                

Abstract

We report herein a case of isolated Rosai-Dorfman disease (Sinus Histiocytosis with Massive Lymphadenopathy) diagnosed upon routine microscopic examination of tonsils in a child. The patient is a 4 year old girl who had a history of sleep apnea, but no other significant medical history or other findings on physical examination. In this report, we discuss the various approaches to handling of tonsillectomy specimens. We also discuss the value of routine microscopic examination, providing a list of case examples of incidental, clinically important, findings that can be missed if a microscopic examination of tonsils was not performed. We finally discuss the clinical significance of finding histologic evidence of Rosai-Dorfman disease in a child.

Keywords

Tonsils; Rosai-Dorfman Disease; Microscopic Examination

Conflicts of Interest

The authors declare no conflicts of interest.

References

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