Renal Pleomorphic Sarcoma in Polycystic Kidney Disease: Case Report

N. Cherif Idrissi El Ganouni, M. Ouali Idrissi, Karima Jiddi, Z. Dahami, F. Barjani, I. Sarf, B. Belaabidia, O. Essadki, A. Ousehal

Department of Pathology, University Hospital Mohammed VI, Marrakesh, Morocco.
Department of Radiology, University Hospital Mohammed VI, Marrakesh, Morocco.
Department of Urology, University Hospital Mohammed VI, Marrakesh, Morocco.

DOI: 10.4236/ojrad.2012.23012                

Abstract

We report a case of pleomorphic sarcoma in a 42-year-old man with adult polycystic kidney disease [APKD]. Abdominal ultrasonography, computed tomography and MRI scans have revealed heterogenous bilateral renal cysts with a voluminous mass in the upper pole left kidney. Radical left nephrectomy with histopathologic and immunohistologic examination have confirmed the diagnosis of pleomorphic sarcoma. Sarcoma associated with adult polycystic kidney disease is extremely rare and does not have particular radiological or biological features when compared to primary renal sarcoma.

Keywords

Polycystic Kidney Disaese; Pleomorphic Sarcoma

Conflicts of Interest

The authors declare no conflicts of interest.

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