Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options

Hafida Benhammane, Leila Chbani, Abdelmalek Ousadden, Ouadii Mouquit, Siham Tizniti, Afaf Riffi Amarti, Nouafal Mellas, Omar El Mesbahi

Department of general surgery, Hassan II University Hospital, Fez, Morocco.
Department of medical oncology, Hassan II University Hospital, Fez, Morocco.
Department of pathology, Hassan II University Hospital, Fez, Morocco.
Department of radiology, Hassan II University Hospital, Fez, Morocco.

DOI: 10.4236/health.2012.44031                

Abstract

Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive variety of sarcoma arising typically from abdominal or pelvic peritoneum. Diagnosis and treatment approaches of this entity are complex and require a skilled, experienced, multidisciplinary team. Authors report their experience with a case of an intraabdominal DSRCT arising in a 37-year-old young man in order to discuss the clinico-pathological and radiological behavior of this tumor and underline diagnostic and therapeutic difficulties.

Keywords

Desmoplastic Small Round Cell Tumor; Abdomen; Histology; Chemotherapy; Surgery; Outcome

Conflicts of Interest

The authors declare no conflicts of interest.

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