TITLE:
Extra Dural Hematoma of the Dorso-Lumbar Region in a Hemophiliac: A Rare Entity
AUTHORS:
Hanane Hajaj, Hanae Bahari, Ayyad Ghanam, Aziza El Ouali, Abdeladim Babakhouya, Maria Rkain
KEYWORDS:
Extradural Hematoma, Children, Hemophilia
JOURNAL NAME:
Open Journal of Pediatrics,
Vol.14 No.1,
January
12,
2024
ABSTRACT: Introduction and objective: Hemophilia is a genetic bleeding disorder inherited as a recessive train linked
to the male gender. Bleeding into the central nervous system in patients with hemophilia is
an extremely dangerous condition that can be directly life-threatening, if left
untreated. Extradural hematoma of the
dorso-lumbar region is rare but potentially deadly disease in children. This condition can result in severe neurological deficits. We aim to discuss the clinical, radiological and
progressive clinical aspects of this illness. Case report: We report the case of a 5-year-old child with severe hemophilia A treated
for extradural hematoma of the
dorso-lumbar region resulting from trauma. A spinal magnetic resonance
imaging revealed an extradural hematoma. The patient was successfully treated
with intensive replacement therapy and did not require surgical intervention. Conclusion: Extradural hematoma is a rare complication of hemophilia, that
needs to be looked for in children who have bleeding disorders. For the best
neurological outcome, early diagnosis is crucial.