TITLE:
Anesthetic Management for a Patient of Gorham’s Syndrome: The Vanishing Bone Disease
AUTHORS:
Aiji Sato-Boku, Eisuke Kako, Megumi Harima, Jun Harada, Kazuya Sobue
KEYWORDS:
Gorham’s Syndrome, Massive Osteolysis, General Anesthesia, Airway Evaluation
JOURNAL NAME:
Open Journal of Anesthesiology,
Vol.7 No.6,
June
19,
2017
ABSTRACT: Gorham-Stout (GS) syndrome or the vanishing bone disease is a very rare chronic disease characterized by the destruction of the osseous matrix and proliferation of vascular structures. Review of the general anesthesia showed only a few cases till date. We report general anesthesia for tooth extraction in a 21-year-old male patient with Gorham-Stout syndrome. In this case, the most concerning issue was limited mouth opening due to mandible osteolysis and difficult intubation was anticipated. To anticipate difficult airway management, it is very important to consider the preoperative airway assessment including the cervical spine screening. In this case, the McGrath video laryngoscope prevented the anticipated difficult intubation due to the limited mouth opening due to mandible osteolysis.