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Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome

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DOI: 10.4236/ojanes.2015.52007    3,673 Downloads   4,122 Views   Citations

ABSTRACT

Hermansky-Pudlak Syndrome (HPS) is a rare genetic condition characterized by platelet function abnormalities and oculocutaneous albinism. Other systemic manifestations of the disease include pulmonary fibrosis, granulomatous colitis, impaired renal function, and cardiomyopathy. Due to the systemic extent of the disease, HPS has multiple anesthetic concerns and requires a detailed preoperative evaluation and close perioperative monitoring.

Conflicts of Interest

The authors declare no conflicts of interest.

Cite this paper

Zach, K. and Misra, L. (2015) Anesthetic Management of a Patient with Hermansky-Pudlak Syndrome. Open Journal of Anesthesiology, 5, 33-36. doi: 10.4236/ojanes.2015.52007.

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