Isolated Mediastinal Lymphangioma: Prenatal Diagnosis and Thoracoscopic Treatment

Francois Varlet, Emmanuelle Guye, Marie Noelle Varlet, Tronchet Mireille, Mariat Guillaume, Chene Gautier

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DOI: 10.4236/ss.2010.11004                

Abstract

Isolated mediastinal lymphangiomas are uncommon. We report a case of a 14 × 8 mm right paracardiac cyst diagnosed at 20 weeks’ gestation. The prenatal evolution was uneventful and a magnetic resonance imaging at 31 weeks showed the limited extension of the cyst into the anterior mediastinum. At birth, the baby was asymptomatic, but the size of the lesion increased steadily (48 × 29 mm). At 7 months of life, he underwent a thoracoscopic resection of the cyst without intra or postoperative complications. Histological examination showed a lymphangioma. This case is remarkable for its prenatal diagnosis, the thoracoscopic treatment and the 8 years of followup without recurrence.

Keywords

Mediastinal Tumor; Mediastinal Lymphangioma; Thoracoscopic Treatment; Prenatal Diagnosis

Conflicts of Interest

The authors declare no conflicts of interest.

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