Author(s)

Amanda Vilaverde Perez¹, Cilomar Martins de Oliveira Filho¹, Tássia Cividanes Pazinato¹, Mariana Sbaraini¹, Edimárlei Gonsales Valério^1,2, Sheila Nogueira do Amaral³, Fernanda Grossi², Daniela Vanessa Vettori^1,2, Janete Vettorazzi^1,2*

¹Obstetrics and Gynecology, Hospital de Clínicas de Porto Alegre, Porto Alegre, Brazil.
²Postgraduation Program in Health Sciences: Gynecology and Obstetrics, Universidade Federal do Rio Grande do Sul, Porto Alegre, Brazil.
³Hematology, Hospital de Clínicas de Porto Alegre, Porto Alegre, Brazil.

Background: Bernard-Soulier Syndrome (BSS) is a rare autosomal recessively inherited bleeding disorder of platelet function. Pregnancy in BSS is associated with a high risk of serious bleeding for both mother and neonate, and current data show no consensual approach. Aim: To report the case of a pregnant woman with BSS, in order to provide more information about management of these cases. Case Presentation: This case report describes a successful pregnancy outcome in a woman with BSS who was closely monitored throughout pregnancy and postpartum period, and had a judiciously planned birth. Conclusion: Management of BSS during pregnancy is still unclear. However, it is important to strictly control platelet counts and plan the birth in advance.

Bernard-Soulier, Hemostasis, Thrombocytopenia, Pregnancy, Obstetrics, Postpartum Hemorrhage

Perez, A. , de Oliveira Filho, C. , Pazinato, T. , Sbaraini, M. , Valério, E. , do Amaral, S. , Grossi, F. , Vettori, D. and Vettorazzi, J. (2019) Bernard-Soulier Syndrome in Pregnancy: A Case Report. Open Journal of Obstetrics and Gynecology, 9, 838-844. doi: 10.4236/ojog.2019.96082.